Abstract: Intestinal Neuronal Dysplasia (IND) is a bowel motility disorder, consisting two distinct clinicopathologic subtypes one manifesting itself as intermittent diarrhea and the other as chronic constipation. We report a patient with intermittent diarrhea and failure to thrive who have a pseudo-obstruction which finally led to the diagnosis of a Intestinal neuronal dysplasia. A review of literature is presented to elucidate the differential diagnosis of the neuronal intestinal dysplasia and pseudo obstruction.