Abstract: Congenital scoliosis is a multifactorial spine deformity with some other coexisting anomalies that can be prevented and possibly relatively corrected by means of individualized operative treatment. To assess different aspects of congenital scoliosis in order to propose optimal preventive as well as corrective operational individualized techniques to reach the optimal outcome. Of 105 consecutive scoliotic patients presenting to Tabriz Shohada Orthopedics Hospital since 2003 to 2005, 35 cases were congenital scoliosis and they form the basis of this study. All cases were thoroughly and meticulously examined and Para-clinically assessed for the spinal deformity, co-existing anomalies, operative strategies, curative out comes and the resulted complications. Fifteen male and 20 female were studied through this survey, with the age range of 2-17 years. The average follow-up was 21 months. Associated kyphosis was seen in 19 (54.28%) patients. Amongst 5 different patterns of curve presentation Hemivertebrae was found to be the commonest type of vertebral anomaly (31.42%). General abnormalities were seen in 25 (73.5%) patients. Genitourinary anomalies were seen in 3 (8.57%) patients. Cardiovascular anomalies were seen in 5 patients (14.28%) with Mitral valve prolapse being the commonest anomaly. In coronal plane the greatest angle before operation was 110 and the least one 50 with mean degree of 72.22 and the mean correction degree of 68.09% in coronal plane. We found one case of hypokyphosis; however, the associated hyperkyphosis was corrected during the operation.